Protein Details: Gamma-aminobutyric acid receptor subunit alpha-5

Protein ID

ICDB_Pro_0479

Protein Name

Gamma-aminobutyric acid receptor subunit alpha-5

Gene Name

GABRA5

Organism

Homo sapiens (Human)

Length

462 amino acids

AlphaFoldDB

AF-P31644-F1-model_v4.pdb

Function

Alpha subunit of the heteropentameric ligand-gated chloride channel gated by gamma-aminobutyric acid (GABA);a major inhibitory neurotransmitter in the brain. GABA-gated chloride channels;also named GABA(A) receptors (GABAAR);consist of five subunits arranged around a central pore and contain GABA active binding site(s) located at the alpha and beta subunit interface(s). When activated by GABA;GABAARs selectively allow the flow of chloride anions across the cell membrane down their electrochemical gradient. GABAARs containing alpha-5/GABRA5 subunits are mainly extrasynaptic and contribute to the tonic GABAergic inhibition in the hippocampus (By similarity). Extrasynaptic alpha-5-containing GABAARs in CA1 pyramidal neurons play a role in learning and memory processes (By similarity).

Sequence

MDNGMFSGFIMIKNLLLFCISMNLSSHFGFSQMPTSSVKDETNDNITIFTRILDGLLDGYDNRLRPGLGERITQVRTDIYVTSFGPVSDTEMEYTIDVFFRQSWKDERLRFKGPMQRLPLNNLLASKIWTPDTFFHNGKKSIAHNMTTPNKLLRLEDDGTLLYTMRLTISAECPMQLEDFPMDAHACPLKFGSYAYPNSEVVYVWTNGSTKSVVVAEDGSRLNQYHLMGQTVGTENISTSTGEYTIMTAHFHLKRKIGYFVIQTYLPCIMTVILSQVSFWLNRESVPARTVFGVTTVLTMTTLSISARNSLPKVAYATAMDWFIAVCYAFVFSALIEFATVNYFTKRGWAWDGKKALEAAKIKKKREVILNKSTNAFTTGKMSHPPNIPKEQTPAGTSNTTSVSVKPSEEKTSESKKTYNSISKIDKMSRIVFPVLFGTFNLVYWATYLNREPVIKGAASPK

PDB Structures

Ligand Binding

1. DICL_CP

2. DICL_Pep

Binding Site

BINDING 101; /ligand="4-aminobutanoate": "ligand shared with the neighboring beta subunit GABRB3"; BINDING 164; /ligand="4-aminobutanoate": "ligand shared with the neighboring beta subunit GABRB3"

Disease

Developmental And Epileptic Encephalopathy and Non-Specific Early-Onset Epileptic Encephalopathy

Location

DOI ID

10.1042/bst020018s; 10.1093/hmg/2.2.183; 10.1038/ng1285; 10.1101/gr.2596504; 10.1006/geno.1997.4770; 10.1073/pnas.0307231101; 10.1002/pmic.200600410; 10.1038/s41422-018-0077-8; 10.1093/braiwy171; 10.1093/braiwz123

RefSeq

NP_000801.1; NP_001158509.1; XP_005268315.1; XP_006720522.1

Feature